Last Updated: February 18, 2025
Amino Acid Biosynthesis and Catabolism
- Foundational Biochemistry
-
Biochemistry Topics
- Carbohydrate Metabolism
- Biochemical Properties of Carbohydrates
- Glycolysis and the Regulation of Blood Glucose
- Fructose Metabolism
- Galactose Metabolism
- Gluconeogenesis
- Glycogen Metabolism
- Pentose Phosphate Pathway
- Ethanol (Alcohol) Metabolism: Acute and Chronic Toxicities
- Glycosaminoglycans and Proteoglycans
- NADPH: Reductive Biosynthesis and Cellular Redox Control
- Lipid Metabolism
- Biochemical Properties of Lipids
- Synthesis of Fatty Acids
- Synthesis of Triglycerides
- Synthesis of Phospholipids
- Lipolysis and the Oxidation of Fatty Acids
- Cholesterol: Synthesis, Metabolism, and Regulation
- Bile Acid Synthesis, Metabolism, and Biological Functions
- Omega-3 and Omega-6 Fatty Acid Synthesis, Metabolism, Functions
- Eicosanoid Metabolism: Prostaglandins, Thromboxanes, Leukotrienes, and Lipoxins
- Sphingolipid Metabolism and the Ceramides
- Bioactive Lipids and Lipid Sensing Receptors
- Bioactive Lipid Mediators of Inflammation
- Lipoproteins, Blood Lipids, and Lipoprotein Metabolism
- Ethanol (Alcohol) Metabolism: Acute and Chronic Toxicities
- Endocannabinoids in Feeding Behavior and Energy Homeostasis
- Krill Oil: Nutritional Benefits
- Amino Acids and Proteins
- Nucleic Acid Biochemistry
- Nitrogen Metabolism
- Iron and Copper Homeostasis
- Energy Generating Processes
- Carbohydrate Metabolism
-
Cellular & Molecular Biology
- Cell Cycles
- Cellular Structure & Organization
- Control of Gene Expression
- DNA, RNA, and Protein Metabolism
- Signal Transduction Processes
- Growth Factors and Other Cellular Regulators
- Secreted Factors: Tissue “Kines”
- Signal Transduction Pathways: Overview
- Signal Transduction Pathways: G-Proteins and GPCR
- Signal Transduction Pathways: MAP Kinases
- Signal Transduction Pathways: PKC Family
- Signal Transduction Pathways: Cyclic Nucleotides and Kinases
- Signal Transduction Pathways: Nucleotides
- Signal Transduction Pathways: Phosphatases
- Signal Transduction Pathways: Phospholipids
- Signal Transduction by Wnt, TGF-β, and BMP
- Farnesoid X Receptors, FXRs
- Liver X Receptors, LXRs
- Peroxisome Proliferator-Activated Receptors, PPARs
- PPAR gamma (PPARγ) Coactivator-1 (PGC-1) Family
- Specialized Enzymes
- Tools of Molecular Medicine
-
Specialized Topics
- Adipose Tissue & Obesity
- Biochemistry of the Nervous System
- Cancer
- Gut & Brain Interactions
- Regulation of Feeding Behaviors
- Hemostasis: Blood Coagulation
- Hormones: Steroid & Peptide
- Insulin & Diabetes
- Muscle Biochemistry
- Nutrition
- Renal Biochemistry
- Specialized Enzymes
- Hypoxia and Metabolism
- Plant-Based Therapeutics
-
Diseases and Disorders
- Congenital Disorders of Glycosylation
- Connective Tissue Disorders
- Disorders of Red Blood Cells
- Disorders of Coagulation Factors
- Diseases Associated with DNA Abnormalities
- Diseases of Amino Acid and Organic Acid Metabolism
- Organic Acidurias/Acidemias
- Alkaptonuria
- Branched-Chain Amino Acid Metabolism Disorders
- Cystinuria
- Glutaric Aciduria Type 1
- Hartnup Disorder
- Homocysteinemia / Homocystinuria
- Isovaleric Acidemia
- Lysinuric Protein Intolerance (LPI)
- Maple Syrup Urine Disease (MSUD)
- Methylmalonic Acidemias/Acidurias
- Phenylketonuria: PKU
- Propionic Acidemia
- Tyrosinemia
- Diseases of Carbohydrate Metabolism
- Glycogen Storage Diseases
- Fructose Metabolism Disorders
- Galactose Metabolism Disorders
- Glucose-6-Phosphate Dehydrogenase (G6PD) Deficiency
- Pyruvate Kinase Deficiency: Erythrocyte
- GLUT1 Deficiency Syndrome, GLUT1DS
- Lafora Disease
- Pyruvate Carboxylase Deficiency
- Pyruvate Dehydrogenase Complex Deficiencies
- Diseases of Cholesterol and Lipoprotein Metabolism
- Familial Hypercholesterolemia (FH)
- Abetalipoproteinemia, ABL: MTTP mutations
- Familial Chylomicronemia Syndrome
- Familial Combined Hypolipidemia: ANGPTL3 mutations
- Familial Hypobetalipoproteinemia Syndrome, FHBL: APOB truncation mutations
- Familial Hypobetalipoproteinemia Syndrome, FHBL: PCSK9 loss-of-function mutations
- Familial LCAT Deficiency: FLD (Fish Eye Disease)
- Lipoprotein(a) and Atherogenesis
- Smith-Lemli-Opitz Syndrome, SLOS
- Tangier Disease: Familial High-Density Lipoprotein Deficiency
- Diseases of Hormone Synthesis or Function
- Disorders of Fatty Acid Metabolism
- Carnitine Deficiency, Systemic Primary
- Carnitine Palmitoyltransferase 2 (CPT2) Deficiency
- Carnitine Palmitoyltransferase 1 (CPT1) Deficiency
- Fatty Acid Oxidation Disorders
- Lipid Storage Myopathies
- Medium Chain Acyl-CoA Dehydrogenase (MCAD) Deficiency
- Short Chain Acyl-CoA Dehydrogenase (SCAD) Deficiency
- Very Long Chain Acyl-CoA Dehydrogenase (VLCAD) Deficiency
- Disorders of Metal Transport and Metabolism
- Disorders of Mucopolysaccharide Metabolism
- Disorders of Nucleotide Metabolism
- Disorders of Oxidative Phosphorylation
- Disorders of Peroxisome Biogenesis and Function
- Urea Cycle Disorders
- Disorders of Glycoprotein and Glycolipid Degradation
- Aspartylglucosaminuria, AGU
- Fabry Disease
- Farber Lipogranulomatosis
- Fucosidosis
- Galactosialidosis (Goldberg Sydrome)
- Gaucher Disease
- GM1 Gangliosidosis
- GM2 Activator Deficiency (Tay-Sachs AB Variant)
- I-Cell Disease, Mucolipidosis II
- Krabbe Disease
- Metachromatic Leukodystrophy, MLD
- Niemann-Pick Diseases
- Pseudo-Hurler Polydystrophy, Mucolipidosis III
- Sandhoff Disease
- Sialidosis
- Tay-Sachs Disease
- Alpha(α)-Mannosidosis
- Beta(β)-Mannosidosis
- Porphyrias and Bilirubinemias
- Acute Intermittent Porphyria, AIP
- ALA Dehydratase Deficient Porphyria, ADP
- Congenital Erythropoietic Porphyria, CEP
- Crigler-Najjar Syndromes
- Dubin-Johnson Syndrome
- Erythropoietic Protoporphyria, EPP
- Gilbert Syndrome
- Hereditary Coproporphyria, HCP
- Porphyria Cutanea Tarda, PCT
- Rotor Syndrome
- Variegate Porphyria, VP
- X-Linked Sideroblastic Anemia, XLSA
- Neuromuscular Disorders
- Alpha Listing – Diseases And Disorders
-
Resources Pages
- Recommended Newborn Screening Panel
- Common Blood Analysis Data
- Abbreviations Used in The Medical Biochemistry Page
- Glossary of Terms used in The Medical Biochemistry Page
- References Used in The Medical Biochemistry Page
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