Disorders in Mitochondrial β-Oxidation

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Very-Long-Chain Acyl-CoA Dehydrogenase Deficiency - VLCAD

Long-Chain Acyl-CoA Dehydrogenase Deficiency - LCAD

Medium-Chain Acyl-CoA Dehydrogenase Deficiency - MCAD

Short-Chain Acyl-CoA Dehydrogenase Deficiency - SCAD

Carnitine Translocase Deficiency

Carnitine Palmitoyltransferase I (CPT I) Deficiency

Carnitine Palmitoylransferase II (CPT II) Deficiency


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Michael W. King, Ph.D / IU School of Medicine / miking at iupui.edu

Last modified: April 22, 2008